Prevalence of congenital heart defects in patients with Down's syndrome.

نویسنده

  • Kemal Nisli
چکیده

Down’s syndrome (DS) is the most frequent chromosomal aberration among newborns, with an incidence of 1/660 live births; trisomy 21 occurs in 95% of cases due to maternal meiosis I non-disjunction, resulting in three full copies of chromosome 21 in each cell. Of these cases, 4% are due to parental/de novo translocation and 1% is due to mosaicism. Frequency of congenital heart defects (CHDs) in children with DS varies greatly in the literature, from 20 to over 60%.1,2

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

The Prevalence of Celiac Disease in Down syndrome Children with and without Congenital Heart Defects

Background The prevalence of celiac disease (CD) is remarkably varied in Down syndrome(DS)patientscompared with other diseases.  This study aimed to assess celiac disease prevalence in Down syndrome children with and without congenital heart defects (CHD) and its comparison with controls. Materials and Methods This case-control study was performed at a single center on 132 participants in three...

متن کامل

Congenital heart defects are under-recognised in adult patients with Down's syndrome.

BACKGROUND Congenital heart defects (CHD) are common in patients with Down's syndrome; however, patients living in residential centres have not always been screened for CHD in the past. The aim of this study was to investigate the prevalence of CHD in patients with Down's syndrome living in residential centres, and to determine whether cardiac screening should be recommended. METHODS Between ...

متن کامل

Heart defects and ocular anomalies in children with Down's syndrome.

AIMS To investigate whether ocular anomalies are associated with congenital heart defects in children with Down's syndrome. METHODS 58 children with Down's syndrome were entered into a retrospective observational study. Children were assigned to heart defect groups based on medical records. Optometric tests had previously been carried out at the homes of the children. RESULTS A relation bet...

متن کامل

Congenital Heart Disease in Children with Down syndrome in Kermanshah, West of Iran during 2002 - 2016

Background Down syndrome is the most common chromosomal anomaly. Dysmorphic features can occur in several organs in this syndrome. Cardiac anomalies with a prevalence of 50% are the most common anomalies responsible for death during the first two years of life. We aimed to determine the prevalence of cardiac anomalies among Down syndrome patients admitted to two tertiary hospitals in Kermanshah...

متن کامل

Study of the Association between Congenital Heart Defects and Neuroblastoma in Abdominal Sonography

Abstract Background A higher prevalence of congenital heart defects (CHD) in neuroblastoma patients in general population is reported in some publications, however, some authors did not find such an association. The evidence for this relation comes from the observation that, the neural crest cells accompany to the development of the heart and neuroblastoma as well. Materials and Methods We...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Jornal de pediatria

دوره 85 5  شماره 

صفحات  -

تاریخ انتشار 2009